Aplasia cutis congenita is a rare congenital disease showing focal abscence of skin. In the majority of instances it is limited to the scalp especially on the vertex although other areas of the body may also be involved. Other congenital
malformation
have been reported to occur with ACC occasionally Diagnosis depends on primarily clinical findings. The histologic finding varies from an absence of appendages to the involvement of varying layers of skin, occasionally extending to the bone or
dura.
Healed lesions often demonstrate a flattened epidermis, a proliferation of fibroblasts in a loose connective tissue stroma, newly formed capillaries, and a complete absence of adnexal structures.
We observed a newborn infant with aplasia cutis congenita. The skin defect was found on the posterior fontanelle. No associating congenital anomalies were found in this case. (Kor J Dermatol 1994 ; 32(4) : 698~702)
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